RESUMO
La esclerosis sistémica (ES) en una enfermedad autoinmune, crónica, multifactorial y sistémica que afecta al tejido conectivo. Presentamos este caso clínico dado la baja prevalencia de ES difusa con compromiso cardíaco temprano y progresivo en una paciente joven, y tratamiento con trasplante cardíaco (AU)
Systemic sclerosis (SS) in a multifactorial and systemic, chronic, autoimmune disease that affects the connective tissue. We present this clinical case given the low prevalence of diffuse SS with early and progressive cardiac compromise in a young patient, and treatment with cardiac transplantation (AU)
Assuntos
Humanos , Feminino , Adulto , Esclerodermia Difusa/complicações , Esclerodermia Difusa/diagnóstico , Esclerodermia Difusa/cirurgia , Transplante de Órgãos/métodos , Transplante de Coração/instrumentação , Transplante de Coração/métodos , Doenças Autoimunes/complicações , Análise MultivariadaRESUMO
Systemic sclerosis (SS) in a multifactorial and systemic, chronic, autoimmune disease that affects the connective tissue. We present this clinical case given the low prevalence of diffuse SS with early and progressive cardiac compromise in a young patient, and treatment with cardiac transplantation.